Pleomorphic Dermal Sarcoma: a case report

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Published: Dec 4, 2023
DOI: https://doi.org/10.52600/2763-583X.bjcr.2024.4.1.66-71
Keywords:
Undifferentiated pleomorphic sarcoma, Pleomorphic dermal sarcoma, Atypical fibroxanthoma, Photodamaged skin

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Carmen Déa Ribeiro de Paula
Dermatology residency service at the University Hospital of Brasilia, University of Brasília
https://orcid.org/0000-0001-8948-992X
Carolina Bezerra Benévolo Abbud
Dermatology residency service at the University Hospital of Brasilia, University of Brasília
https://orcid.org/0000-0002-0950-1077
Luiz Eduardo de Almeida Prado Franceschi
Laboratório Diagnose
Aridne Souza Costa Campos
Dermatology residency service at the University Hospital of Brasilia, University of Brasília
https://orcid.org/0000-0001-8261-1662
Lucas Frizon Greggianin
Dermatology residency service at the University Hospital of Brasilia, University of Brasília
https://orcid.org/0009-0006-6744-4214
Isadora Ataide Caldeira
Dermatology residency service at the University Hospital of Brasilia, University of Brasília
https://orcid.org/0000-0003-3305-5553
Vanessa Queiroz Bastos
Dermatology residency service at the University Hospital of Brasilia, University of Brasília
https://orcid.org/0000-0003-1241-4393
Juliana Tomaz Esper
Dermatology residency service at the University Hospital of Brasilia, University of Brasília
https://orcid.org/0000-0002-3982-2306

Abstract

This case report brings a 79-year-old man, with a history of melanoma in situ on the extensor part of the left arm, who presented with an ulcerated nodule on the scalp, right parietal region, with rapid and progressive growth for 3 months. The lesion was clinically compatible with squamous cell carcinoma, Merkel carcinoma, amelanotic melanoma and pleomorphic dermal sarcoma. Exeresis was performed and the diagnosis of Pleomorphic Dermal Sarcoma (PDS) was confirmed by histological and immunohistochemical evaluation. Pleomorphic Dermal Sarcoma (PDS), formerly known as malignant fibrous histiocytoma or undifferentiated pleomorphic sarcoma of the skin, is a rare spindle cell mesenchymal tumor that may recur locally or metastasize. Our objective is to present this rare tumor to the reader, discussing the clinical, histological and immunohistochemical presentation, and to highlight the need for further studies on surgical management protocols and the development of guidelines for the standardization of management and safe follow-up of these patients.

Article Details

How to Cite
Paula, C. D. R. de, Abbud, C. B. B., Franceschi, L. E. de A. P., Campos, A. S. C., Greggianin, L. F., Caldeira, I. A., Bastos, V. Q., & Esper, J. T. (2023). Pleomorphic Dermal Sarcoma: a case report. Brazilian Journal of Case Reports, 4(1), 66–71. https://doi.org/10.52600/2763-583X.bjcr.2024.4.1.66-71
Issue
Vol. 4 No. 1 (2024): January/March - 2024
Section
Clinical Case Reports
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This work is licensed under a Creative Commons Attribution 4.0 International License.

Author Biographies

Carmen Déa Ribeiro de Paula, Dermatology residency service at the University Hospital of Brasilia, University of Brasília

Dermatology residency service at the University Hospital of Brasilia, University of Brasília, Brasília, Brazil.

Carolina Bezerra Benévolo Abbud, Dermatology residency service at the University Hospital of Brasilia, University of Brasília

Dermatology residency service at the University Hospital of Brasilia, University of Brasília, Brasília, Brazil.

Luiz Eduardo de Almeida Prado Franceschi, Laboratório Diagnose

Laboratório Diagnose, Brasília, Brazil.

Aridne Souza Costa Campos, Dermatology residency service at the University Hospital of Brasilia, University of Brasília

Dermatology residency service at the University Hospital of Brasilia, University of Brasília, Brasília, Brazil.

Lucas Frizon Greggianin, Dermatology residency service at the University Hospital of Brasilia, University of Brasília

Dermatology residency service at the University Hospital of Brasilia, University of Brasília, Brasília, Brazil.

Isadora Ataide Caldeira, Dermatology residency service at the University Hospital of Brasilia, University of Brasília

Dermatology residency service at the University Hospital of Brasilia, University of Brasília, Brasília, Brazil.

Vanessa Queiroz Bastos, Dermatology residency service at the University Hospital of Brasilia, University of Brasília

Dermatology residency service at the University Hospital of Brasilia, University of Brasília, Brasília, Brazil.

Juliana Tomaz Esper, Dermatology residency service at the University Hospital of Brasilia, University of Brasília

Dermatology residency service at the University Hospital of Brasilia, University of Brasília, Brasília, Brazil.

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